H Syndrome: Two new morrocan cases

H Syndrome is a rare genodermatosis of autosomal recessive inheritance characterised by the presence cutaneous and systemic manifestations. This syndrome due to mutation in SLC9A3 gene encoding hENTt3 transport protein. Still little known rare, its diagnosis difficult. Nearly 100 cases have been described, majority which were from Arab countries. The possible occurrence other undiagnosed or misdiagnosed highly probable common features shared with syndromes. We report two new Morocco. One them presents unique association celiac disease has not previously reported. dermatologist’s main goal diagnose condition enable appropriate follow-up genetic counselling.